Glycoproteinosis are lysosomal storage diseases affecting glycoproteins, resulting from defects in lysosomal function. The term is sometimes reserved for conditions involving degradation of glycoproteins.

__TOC__ Types (E77.0) Defects in post-translational modification of lysosomal enzymes Mucolipidosis II (I-cell disease) Mucolipidosis III (pseudo-Hurler polydystrophy) (E77.1) Defects in glycoprotein degradation Aspartylglucosaminuria Fucosidosis Mannosidosis Sialidosis (mucolipidosis I)

Another type, recently characterized, is galactosialidosis.

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NIH