IgG4-related skin disease is the recommended name for skin manifestations in IgG4-related disease (IgG4-RD). Multiple different skin manifestations have been described.
Classification Although a clear understanding of the various skin lesions in IgG4-related disease is a work in progress, skin lesions have been classified into subtypes based on documented cases: Angiolymphoid hyperplasia with eosinophilia (or lesions that mimic it) and cutaneous pseudolymphoma Cutaneous plasmacytosis Eyelid swelling (as part of Mikulicz's disease) Psoriasis-like eruptions Unspecified maculopapular or erythematous eruptions Hypergammaglobulinemic purpura and urticarial vasculitis Impaired blood supply to fingers or toes, leading to Raynaud's phenomenon or gangrene
In addition, Wells syndrome has also been reported in a case of IgG4-related disease. See also IgG4-related disease
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